Knowra Ebstein's anomaly Ebstein's anomaly Ebstein's anomaly is a congenital heart defect in which the tricuspid valve is displaced toward the right ventricle. The displacement can cause valve leakage, atrial enlargement, and abnormal heart rhythms.
Tricuspid valve : The heart valve between the right atrium and right ventricle, preventing blood from flowing backward during ventricular contraction. Its downward displacement and malformed leaflets define the defect.
Echocardiography : Ultrasound imaging that shows the heart's structure, motion, and blood flow. It identifies valve displacement, leakage, chamber size, and ventricular function.
Congenital heart defect : A structural abnormality of the heart or great vessels that is present at birth. Ebstein's anomaly belongs to this broad class of developmental disorders.
Carpentier classification : A surgical classification of Ebstein's anomaly based on valve displacement and the size of the functional right ventricle. It links anatomic severity to operative planning.
Atrialization of the right ventricle : The portion of the right ventricle above the displaced tricuspid valve, which functions more like part of the right atrium. This distinctive remodeling reduces the effective pumping chamber.
Electrocardiography : A recording of the heart's electrical activity using electrodes placed on the skin. It can reveal conduction abnormalities, pre-excitation, and arrhythmias.
Heart development : The embryonic processes that form the heart's chambers, valves, and major vessels. The anomaly originates during formation of the tricuspid valve and right ventricle.
Cone reconstruction : A surgical technique that reconstructs the tricuspid valve from its own leaflets into a cone-shaped valve. It is a specialized repair developed for the malformed valve in this condition.
Tricuspid regurgitation : Backward flow of blood from the right ventricle into the right atrium through an inadequately closing tricuspid valve. Malformed leaflets commonly prevent the valve from sealing.
Cardiac magnetic resonance imaging : Magnetic resonance imaging used to measure heart structure, function, and blood flow. It can quantify right-ventricular size and function when ultrasound is insufficient.
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