KnowraMaple syrup urine diseaseLinked fromLinked fromThe 4 pages that link to Maple syrup urine disease, each with the reason it gives.All 4Broader topic 2Related 2Branched-chain amino acidBroader topic: It is the best-known clinical consequence of defective branched-chain amino acid catabolism.ValineRelated: Impaired breakdown causes valine and related metabolites to accumulate.IsoleucineRelated: Isoleucine and its metabolites accumulate when this pathway is impaired.Metabolic disorderBroader topic: Its characteristic pathway defect can cause dangerous metabolite accumulation.